fig61

Figure 61. An echocardiogram (apical 4-chamber view) of an infant with pulmonary atresia with an intact ventricular septum. Severe tricuspid valve hypoplasia with a severely hypoplastic right ventricle (RV) and a thick myocardium is seen. An arrow indicates the location of an atrial defect. Subsequent imaging with color Doppler showed random color signals in the RV myocardium, raising suspicion of coronary sinusoids. This was confirmed by the angiogram performed later. Reproduced from Ref.^[50]. LA: Left atrium; LV: left ventricle; RA: right atrium.